Arrhythmogenic right ventricular dysplasia - Revision history

Danbot: Add See Also section

2026-03-22T09:25:18Z

Add See Also section

← Older revision		Revision as of 09:25, 22 March 2026
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	**Cardiac arrest in first-degree relative		**Cardiac arrest in first-degree relative
	*Incidental finding: Cardiology follow-up for further risk assessment and possible ICD placement or ablation		*Incidental finding: Cardiology follow-up for further risk assessment and possible ICD placement or ablation

			==See Also==
			*[[Sudden cardiac death]]
			*[[Ventricular tachycardia]]
			*[[Cardiomyopathy]]

	==References==		==References==

Rossdonaldson1: /* Imaging */

2021-03-11T17:39:10Z

Imaging

← Older revision		Revision as of 17:39, 11 March 2021
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	===Imaging===		===Imaging===
			[[File:Arvd MRI.jpg\|thumb\|MRI in a patient affected by ARVC/D (long axis view of the right ventricle): note the transmural diffuse bright signal in the RV free wall on spin echo T1 (a) due to massive myocardial atrophy with fatty replacement (b).]]
	''Major and minor criteria rely on echo and cardiac MRI''		''Major and minor criteria rely on echo and cardiac MRI''
	*[[Echocardiography]]		*[[Echocardiography]]

Rossdonaldson1: /* Background */

2021-03-11T17:37:27Z

Background

← Older revision		Revision as of 17:37, 11 March 2021
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	==Background==		==Background==
			[[File:Arrhythmogenic right ventricular cardiomyopathy.jpg\|thumb\|In vitro MRI and corresponding cross section of the heart in ARVD show RV dilatation with anterior and posterior aneurysms (17-year-old asymptomatic male athlete who died suddenly during a soccer game).]]
	*Second most common cause of sudden cardiac death in young patients <ref>https://litfl.com/arrhythmogenic-right-ventricular-cardiomyopathy-arvc/</ref>		*Second most common cause of sudden cardiac death in young patients <ref>https://litfl.com/arrhythmogenic-right-ventricular-cardiomyopathy-arvc/</ref>
	**Up to 20% of sudden cardiac deaths in young people		**Up to 20% of sudden cardiac deaths in young people

Rossdonaldson1: /* Imaging */

2021-03-11T17:35:13Z

Imaging

← Older revision		Revision as of 17:35, 11 March 2021
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	===Imaging===		===Imaging===
	Major and minor criteria rely on echo and cardiac MRI		''Major and minor criteria rely on echo and cardiac MRI''
	*[[Echocardiography]]		*[[Echocardiography]]
	**Hypokinetic and dilated right ventricle		**Hypokinetic and dilated right ventricle

Rossdonaldson1: /* Evaluation */

2021-03-11T17:33:41Z

Evaluation

← Older revision		Revision as of 17:33, 11 March 2021
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	==Evaluation==		==Evaluation==
	===[[ECG]]===		===[[ECG]]===

	[[File:ARVDV1.png\|thumb\|Epsilon Wave in Lead V1]]		[[File:ARVDV1.png\|thumb\|Epsilon Wave in Lead V1]]
	[[File:ARVD.png\|~~250px~~]]		[[File:ARVD.png\|thumb\|]]
	*Epsilon wave		*Epsilon wave
	**Seen in 30-50% of cases		**Seen in 30-50% of cases

Bobbycarey: /* ECG */

2021-03-10T01:43:29Z

ECG

← Older revision		Revision as of 01:43, 10 March 2021
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	==Evaluation==		==Evaluation==
	===[[ECG]]===		===[[ECG]]===

			[[File:ARVDV1.png\|thumb\|Epsilon Wave in Lead V1]]
	[[File:ARVD.png\|250px]]		[[File:ARVD.png\|250px]]
	*Epsilon wave		*Epsilon wave

ClaireLewis at 14:42, 31 August 2019

2019-08-31T14:42:06Z

← Older revision		Revision as of 14:42, 31 August 2019
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	*[[Palpitations]] (27%)		*[[Palpitations]] (27%)
	*[[Syncope]] (26%)		*[[Syncope]] (26%)
	*Ventricular ~~dysrhythmia~~/[[cardiac arrest]] (23%)		*[[Ventricular dysrhythmias]]/[[cardiac arrest]] (23%)
	**Especially occurring during exercise		**Especially occurring during exercise
	*Family history of unexplained syncope or sudden death		*Family history of unexplained syncope or sudden death
	*Dysrhythmias refractory to ~~anti-dysrhythmic~~ meds		*[[Dysrhythmias]] refractory to antidysrhythmic meds
	*Asymptomatic (40%)		*Asymptomatic (40%)
	**Usually these patients are identified through genetic testing of an affected or symptomatic family member		**Usually these patients are identified through genetic testing of an affected or symptomatic family member
	*Right ventricular failure (6%)		*[[CHF\|Right ventricular failure]] (6%)
	*Dilated cardiomyopathy		*[[Dilated cardiomyopathy]]
	*[[Dyspnea]]		*[[Dyspnea]]
	*Atypical [[chest pain]] (6%)		*Atypical [[chest pain]] (6%)
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	==Evaluation==		==Evaluation==
	===ECG===		===[[ECG]]===
	[[File:ARVD.png\|250px]]		[[File:ARVD.png\|250px]]
	*Epsilon wave		*Epsilon wave
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	===Imaging===		===Imaging===
	Major and minor criteria rely on echo and cardiac MRI		Major and minor criteria rely on echo and cardiac MRI
	*~~Echo~~		*[[Echocardiography]]
	**Hypokinetic and dilated right ventricle		**Hypokinetic and dilated right ventricle
	**Dilation of RVOT		**Dilation of RVOT
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	==Management==		==Management==
	*Beta blockers or amiodarone to suppress ventricular dysrhythmias		*[[Beta blockers]] or [[amiodarone]] to suppress ventricular dysrhythmias
	**Sotalol is preferred		**[[Sotalol]] is preferred
	*ICD implantation if high-risk features		*ICD implantation if high-risk features
	*Ablation of conduction pathways		*Ablation of conduction pathways
	*Treat heart failure with diuretics, ACE inhibitors		*Treat [[heart failure]] with [[diuretics]], [[ACE inhibitors]]
	*Heart transplant		*Heart transplant

SLuckettG: /* Management */

2019-03-20T01:10:26Z

Management

← Older revision		Revision as of 01:10, 20 March 2019
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	==Management==		==Management==
	*Sotalol is ~~the~~ preferred ~~anti~~-~~dysrhythmic~~		*Beta blockers or amiodarone to suppress ventricular dysrhythmias
	*~~Manage~~ heart failure ~~in the usual manner~~		**Sotalol is preferred
			*ICD implantation if high-risk features
			*Ablation of conduction pathways
			*Treat heart failure with diuretics, ACE inhibitors
			*Heart transplant

	==Disposition==		==Disposition==

SLuckettG: /* Disposition */

2019-03-20T01:08:01Z

Disposition

← Older revision		Revision as of 01:08, 20 March 2019
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	==Disposition==		==Disposition==
	*~~Symptomatic presentation~~: ~~Admission~~ to ~~cardiology~~		*Admission under cardiology if symptomatic
			*Admission under cardiology if high-risk features<ref>https://litfl.com/arrhythmogenic-right-ventricular-cardiomyopathy-arvc/</ref>:
			**Syncope due to cardiac arrest
			**Recurrent dysrhythmias not suppressed by drug therapy
			**Cardiac arrest in first-degree relative
	*Incidental finding: Cardiology follow-up for further risk assessment and possible ICD placement or ablation		*Incidental finding: Cardiology follow-up for further risk assessment and possible ICD placement or ablation

SLuckettG: /* Imaging */

2019-03-20T01:06:03Z

Imaging

← Older revision		Revision as of 01:06, 20 March 2019
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	===Imaging===		===Imaging===
	Major and minor criteria rely on echo and cardiac MRI		Major and minor criteria rely on echo and cardiac MRI
	*Echo ~~- hypokinetic~~ and dilated ~~RV, dilation~~ of RVOT		*Echo
	*Cardiac MRI - ~~fibro~~-fatty ~~change with~~ RV ~~myocardial thinning, RV aneurysms,~~ RV dilatation		**Hypokinetic and dilated right ventricle
			**Dilation of RVOT
			*Cardiac MRI <ref>https://litfl.com/arrhythmogenic-right-ventricular-cardiomyopathy-arvc/</ref>
			**Fibro-fatty infiltration
			**Thinning of right ventricular myocardium
			**RV aneurysm
			**RV dilatation
			**Regional wall motion abnormalities
			**Global systolic dysfunction
			*Histological studies provide post-mortem diagnosis
			**May prompt testing in family members

	==Management==		==Management==