Acute intermittent porphyria: Difference between revisions

(Created page with "==Background== ==Clinical Features== ==Differential Diagnosis== ==Diagnosis== ==Management== *Analgesia *Glucose load **Decreases porphyrin production **Typical protocol i...")
 
(Redirected page to Porphyria)
Tag: New redirect
 
(14 intermediate revisions by 5 users not shown)
Line 1: Line 1:
==Background==
#REDIRECT[[Porphyria]]
 
==Clinical Features==
 
==Differential Diagnosis==
 
==Diagnosis==
 
==Management==
*Analgesia
*Glucose load
**Decreases porphyrin production
**Typical protocol is D10W 3-4 liters daily x 4 days
**Risk of hyponatremia given significant free water load
*Hemin
**Decreases porphyrin production, significantly more potent than glucose
**Recommended for most cases requiring hospitalization, or any with neurologic symptoms
**3-4 mg/kg daily for 4 days
**Can cause significant infusion site phlebitis - minimize by reconstituting in 25% albumin; consider central venous administration
**Very expensive - around $8000 per 313 mg vial
==Disposition==
 
==See Also==
 
==External Links==
 
==References==
<references/>

Latest revision as of 17:48, 1 October 2019

Redirect to:

Retrieved from "https://www.wikem.org/w/index.php?title=Acute_intermittent_porphyria&oldid=231350"