Cor triatriatum: Difference between revisions
(Created page with "==Background== *Congenital Anamoly with heart with three atria *Either LA or RA can be divided into 2 compartments (cor triatriatum sinistrum vs cor triatriatum dextrum) *Can...") |
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==Clinical Features== | ==Clinical Features== | ||
*Sinistrum variant most associated with other congenital cardiovascular defects in symptomatic infants | |||
*Can be incidental finding in adults as either isolated finding or in association with PFO, ASD, persistent L superior vena cava | |||
==Differential Diagnosis== | ==Differential Diagnosis== | ||
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==Management== | ==Management== | ||
*As associates with major cyanotic or acyanotic congenital heart lesions, mortality can be up to 75% in untreated symptomatic infants | |||
==Disposition== | ==Disposition== | ||
Revision as of 20:36, 19 April 2016
Background
- Congenital Anamoly with heart with three atria
- Either LA or RA can be divided into 2 compartments (cor triatriatum sinistrum vs cor triatriatum dextrum)
- Can be associated with other congenital syndromes including tetralogy of Fallot, double outlet RV, coarctation of aorta, VSD, AV septal defect
- 0.1-0.4% incidence in USA
Clinical Features
- Sinistrum variant most associated with other congenital cardiovascular defects in symptomatic infants
- Can be incidental finding in adults as either isolated finding or in association with PFO, ASD, persistent L superior vena cava
Differential Diagnosis
Diagnosis
Management
- As associates with major cyanotic or acyanotic congenital heart lesions, mortality can be up to 75% in untreated symptomatic infants