Cor triatriatum: Difference between revisions
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==Background== | ==Background== | ||
*Congenital Anamoly with heart with three atria | *Congenital Anamoly with heart with three atria | ||
*Either LA or RA can be divided into 2 compartments (cor triatriatum sinistrum | *Either LA or RA can be divided into 2 compartments (cor triatriatum sinistrum or cor triatriatum dextrum) | ||
*Can be associated with other congenital syndromes including tetralogy of Fallot, double outlet RV, coarctation of aorta, VSD, AV septal defect | *Can be associated with other congenital syndromes including tetralogy of Fallot, double outlet RV, coarctation of aorta, VSD, AV septal defect | ||
*0.1-0.4% incidence in USA | *0.1-0.4% incidence in USA | ||
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*Sinistrum variant most associated with other congenital cardiovascular defects in symptomatic infants | *Sinistrum variant most associated with other congenital cardiovascular defects in symptomatic infants | ||
*Can be incidental finding in adults as either isolated finding or in association with PFO, ASD, persistent L superior vena cava | *Can be incidental finding in adults as either isolated finding or in association with PFO, ASD, persistent L superior vena cava | ||
*Symptoms depend on size of opening in accessory membrane between the atria | |||
*Symptoms include dyspnea on exertion, orthopnea, easy fatiguability, low exercise tolerance, palpitations | |||
*Increased risk of thrombus formation in LA | |||
==Differential Diagnosis== | ==Differential Diagnosis== | ||
==Diagnosis== | ==Diagnosis== | ||
*Murmur | |||
*Elevated JVD | |||
*Hepatomegaly | |||
*Ascites | |||
*Peripheral edema | |||
*Often discovered on cardiac imaging studies (Echo, Right heart cath) | |||
==Management== | ==Management== | ||
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==References== | ==References== | ||
*MedScape | |||
<references/> | <references/> | ||
Revision as of 20:51, 19 April 2016
Background
- Congenital Anamoly with heart with three atria
- Either LA or RA can be divided into 2 compartments (cor triatriatum sinistrum or cor triatriatum dextrum)
- Can be associated with other congenital syndromes including tetralogy of Fallot, double outlet RV, coarctation of aorta, VSD, AV septal defect
- 0.1-0.4% incidence in USA
Clinical Features
- Sinistrum variant most associated with other congenital cardiovascular defects in symptomatic infants
- Can be incidental finding in adults as either isolated finding or in association with PFO, ASD, persistent L superior vena cava
- Symptoms depend on size of opening in accessory membrane between the atria
- Symptoms include dyspnea on exertion, orthopnea, easy fatiguability, low exercise tolerance, palpitations
- Increased risk of thrombus formation in LA
Differential Diagnosis
Diagnosis
- Murmur
- Elevated JVD
- Hepatomegaly
- Ascites
- Peripheral edema
- Often discovered on cardiac imaging studies (Echo, Right heart cath)
Management
- As associates with major cyanotic or acyanotic congenital heart lesions, mortality can be up to 75% in untreated symptomatic infants
Disposition
See Also
External Links
References
- MedScape