Idiopathic pulmonary fibrosis: Difference between revisions
No edit summary |
No edit summary |
||
| Line 12: | Line 12: | ||
==DDx== | ==DDx== | ||
{{Pulmonary fibrosis differential}} | {{Pulmonary fibrosis differential}} | ||
==Management== | |||
==See Also== | ==See Also== | ||
| Line 17: | Line 20: | ||
==Sources== | ==Sources== | ||
*Bhatti H et al. Approach to acute exacerbation of idiopathic pulmonary fibrosis. Ann Thorac Med. 2013. Vol 8, Issue 2. Pg 71-77. | |||
*Collard HR et al. Acute Exacerbations of Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med. 2007 Oct 1; 176(7): 636–643. | *Collard HR et al. Acute Exacerbations of Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med. 2007 Oct 1; 176(7): 636–643. | ||
*Ryerson CJ et al. Acute exacerbation of idiopathic pulmonary fibrosis: shifting the paradigm. Eur Respir J. 2015 Aug;46(2):512-20. | *Ryerson CJ et al. Acute exacerbation of idiopathic pulmonary fibrosis: shifting the paradigm. Eur Respir J. 2015 Aug;46(2):512-20. | ||
Revision as of 10:13, 13 April 2016
Background
- Median survival time 3 yrs after diagnosis
- Prevalence about 10-20 cases per 100,000 people
- Acute exacerbations carry mortality up to 80%
- 60% die from idiopathic pulmonary fibrosis, others die from:
- VTE
- Cardiovascular (ACS, CHF)
- Infection
Clinical Features
DDx
Pulmonary Fibrosis
- Interstitial pneumonias (acute, lymphocytic)
- Lung malignancy
- Aspiration pneumonia or pneumonitis
- Bacterial, viral, or fungal pneumonia
- Cryptogenic organizing pneumonia
- Interstitial lung disease associated with collagen vascular disease
- Drug-induced pulmonary toxicity (amiodarone, bleomycin, amphotericin B, carbamazepine, etc.)
- Eosinophilic granuloma (Histiocytosis X)
- Radiation pneumonitis
- Sarcoidosis
- Pneumoconiosis (Workplace exposure)
- Asbestosis
- Berylliosis
- Chemical worker's lung
- Coal worker's pneumoconiosis
- Silicosis
Management
See Also
Sources
- Bhatti H et al. Approach to acute exacerbation of idiopathic pulmonary fibrosis. Ann Thorac Med. 2013. Vol 8, Issue 2. Pg 71-77.
- Collard HR et al. Acute Exacerbations of Idiopathic Pulmonary Fibrosis. Am J Respir Crit Care Med. 2007 Oct 1; 176(7): 636–643.
- Ryerson CJ et al. Acute exacerbation of idiopathic pulmonary fibrosis: shifting the paradigm. Eur Respir J. 2015 Aug;46(2):512-20.
- Juarez MM et al. Acute exacerbation of idiopathic pulmonary fibrosis—a review of current and novel pharmacotherapies. J Thorac Dis. 2015 Mar; 7(3): 499–519.